Abstract
Persistent Mullerian duct syndrome (PMDS) is characterized by the presence of a uterus, fallopian tubes and upper vagina in otherwise a phenotypically and genotypically normal male. The embryology, clinical features, diagnosis and aspects of management are discussed.
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Chertin B, Koulikov D, Alberton J. The use of laparoscopy in intersex patients. Pediatr Surg Int. 2006;22:405–8.
Crankson SJ, Bin Yahib S. Persistent Mullerian duct syndrome in a child: surgical management. Anna Saudi Med. 2000;20:267–9.
Guerrier D, Tran D, Vanderwinden JM, Hideux S, Van Outryve L, Legeai L, et al. The persistent Müllerian duct syndrome: a molecular approach. J Clin Endocrinol Metab. 1989;68:46–52.
Josso N, Picard JY, Imbeaud S, Carré-Eusèbe D, Zeller J, Adamsbaum C. The persistent müllerian duct syndrome: a rare cause of cryptorchidism. Eur J Pediatr. 1993;152(Suppl 2):S76–8.
Loeff DS, Imbeaud S, Reyes HM, Meller JL, Rosenthal IM. Surgical and genetic aspects of persistent mullerian duct syndrome. J Pediatr Surg. 1994;29:61–5.
Odi TO, Abdur-Rahman LO, Nasir AA. Persistent Mullerian duct syndrome: a case report and review of the literature. Afr J Paediatr Surg. 2010;7(3):191–3.
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Al-Salem, A.H. (2020). Persistent Müllerian Duct Syndrome (Hernia Uteri Inguinalis). In: Atlas of Pediatric Surgery. Springer, Cham. https://doi.org/10.1007/978-3-030-29211-9_74
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DOI: https://doi.org/10.1007/978-3-030-29211-9_74
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Publisher Name: Springer, Cham
Print ISBN: 978-3-030-29210-2
Online ISBN: 978-3-030-29211-9
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